ย GORLIN SYNDROME (Basal Nevus Cell Carcinoma Syndrome)โญIMPORTANT POINTS TO PONDERGorlin syndrome is an autosomal dominant neurocutaneous (phakomatosis) disease characterized by a triad of multiple basal cell nevi, jaw odontogenic keratocysts, and skeletal anomalies.ย ๐นAn odontogenic (primordial) keratocyst is a cyst that arises from a tooth before its calcification.๐นIt is most commonly located posterior to the premolar region of the mandible or maxilla.๐นIn the mandible, it mostly affects theย third molar tooth.๐นIn men, the disease causes hypogonadism, while in women it causes calcified ovarian fibroids.ย
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